ABSTRACT
Las enfermedades perianales del adulto, de carácter no infeccioso y no neoplásico, son un motivo de consulta poco frecuente. Se caracterizan por la variedad de su etiología y de su sintomatología clínica, y plantean dificultad en el diagnóstico y en la terapéutica. El objetivo del presente trabajo es abordar una patología que plantea la necesidad de una intervención interdisciplinaria. Se incluyen consideraciones anatomopatológicas, clínicas y terapéuticas. (AU)
Noninfectious, non- neoplasic perianal affections are uncommon diseases. They are characterized by the variety of the etiology and clinical symptomatology, posing difficulty in diagnosis and therapeutics. The objective of this paper is to address a pathology that raises the need for interdisciplinary intervention anatomopathological, clinical and therapeutic considerations are included. (AU)
Subject(s)
Humans , Adult , Anus Diseases/diagnosis , Anus Diseases/therapy , Patient Care Team , Skin Diseases, Vesiculobullous/diagnosis , Skin Diseases, Vesiculobullous/therapy , Dermatitis Herpetiformis/diagnosis , Dermatitis Herpetiformis/therapy , Pemphigoid, Benign Mucous Membrane/diagnosis , Pemphigoid, Benign Mucous Membrane/therapy , Pemphigus/diagnosis , Pemphigus/therapy , Stevens-Johnson Syndrome/diagnosis , Stevens-Johnson Syndrome/therapy , Pemphigus, Benign Familial/diagnosis , Pemphigus, Benign Familial/therapy , Dermatitis, Contact/diagnosis , Dermatitis, Contact/therapyABSTRACT
El penfigoide cicatricial o de mucosas es una patología que afecta principalmente a la mucosa oral y ocular. Sólo en 25% de los pacientes afecta también la piel y en alrededor de 10% de los pacientes compromete a la mucosa faringo-laríngea, produciendo en los casos severos disnea que incluso puede requerir traqueostomía. En el tratamiento del penfigoide cicatricial habitualmente se utilizan corticoides e inmunosupresores. En este artículo presentamos un caso de una mujer de 69 años con diagnóstico de penfigoide cicatricial que se manifiesta con disfagia y se comprueba con nasofibroscopía una estenosis supraglótica. Se discute el diagnóstico y manejo de esta patología poco habitual.
Cicatricial or mucous membranes pemphigoid is a rare pathology that affects mainly the ocular and oral mucosae. In only 25% of patients the skin is affected, and in 10%, the pharyngolaryngeal mucosa, resulting in serious cases in dyspnea that could even require a tracheostomy. Treatment is usually based on corticoids and immunosupressors. In this article we present the case of a 69 year old woman diagnosed with cicatricial pemphigoid, that presented dysphagia. A nasoendoscopy revealed supraglottic stenosis. Diagnosis and treatment of this uncommon disease are discussed.
Subject(s)
Humans , Female , Aged , Laryngostenosis/etiology , Pemphigoid, Benign Mucous Membrane/complications , Pemphigoid, Benign Mucous Membrane/diagnosis , Pemphigoid, Benign Mucous Membrane/therapy , Dyspnea/etiology , Deglutition Disorders/etiology , Oral Ulcer/etiologyABSTRACT
The author describes herein a case who presented with deterioration of vision, chronic conjunctivitis and scarring, symblephera formation, obliteration of lacrimal puncti and inferior fornices. To the author's best knowledge, this is the first case of OCP to be reported from Bahrain. Cases of OCP can easily be missed in our part of the world where chronic trachoma is prevalent. The author emphasises the importance of early diagnosis and management of this blinding disorder
Subject(s)
Humans , Female , Eye Diseases , Pemphigoid, Benign Mucous Membrane/therapy , XerophthalmiaABSTRACT
Os autores iniciam o desenvolvimento do tema alteraçoes de tecidos moles da boca, esclarecendo à classe médica sobre as principais doenças vesicobolhosas, condiçoes ulcerativas e lesoes verrucosas papilares.